Ces radiol. 2024, 78(4):214-218 | DOI: 10.55095/CesRadiol2024.030

Zriedkavý prípad difúzneho leptomeningeálneho glioneuronálneho tumoruOriginal article

Simona Kurčinová, Erich Mlčák
Kysucká nemocnica s poliklinikou Čadca (KNsP), Slovenská republika

Diffuse leptomeningeal glioneuronal tumor (DL-GNT) is not a common disease, it has been just lately described as a tumor of the central nervous system. For the first time it was introduced in the 4th edition of WHO classification of CNS tumors in 2014. This type of tumor was categorised into the group of glioneuronal tumors in its current 5th edition of WHO classification of CNS tumors.

The clinical presentation varies according to areas of involvement. The major feature of this tumor as observed in the literature is leptomeningeal involvement with post-contrast enhancement, which secondary may lead to hydrocephalus. Parenchymal components are often not presented. An additional finding is the presence of small subpial cysts, found over the surface of the inferior parts of the supratentorial structures, in the posterior fossa and over the spinal cord.

We present the case of a 19 year old female with leptomeningeal and also pachymeningeal involvement of the spine, with the follow-up also affecting meninges of the brain. What is interesting and worth to mention is that the typical sign of hydrocephalus was not present in our case.

Keywords: central nervous system neoplasms, leptomeningeal neoplasms, magnetic resonance imaging

Accepted: October 10, 2024; Published: December 12, 2024  Show citation

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Kurčinová S, Mlčák E. Zriedkavý prípad difúzneho leptomeningeálneho glioneuronálneho tumoru. Ces radiol. 2024;78(4):214-218. doi: 10.55095/CesRadiol2024.030.
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